Living-donor liver transplant in 3 patients with Budd-Chiari syndrome: case report.
نویسندگان
چکیده
Budd-Chiari syndrome is a rare but life-threatening disorder characterized by obstruction of the hepatic venous outflow. Treatment depends on the underlying cause, the location, and extent of the obstruction, and the functional capacity of the liver. A stepwise therapeutic approach is commonly accepted. When all other therapy options are unsuccessful, or in case of end-stage liver disease, transplant should be considered. We present case reports of 3 patients with Budd-Chiari syndrome who underwent living-donor liver transplant. Characteristic features of Budd-Chiari syndrome, diagnostic and therapeutic interventions, complications, and overall outcomes are discussed. We believe that when a deceased donor graft is unavailable, a living-donor liver transplant can be a safe option for patients with end-stage liver disease associated with Budd-Chiari syndrome.
منابع مشابه
Orthotopic Liver Transplant for Budd-Chiari Syndrome: An Analysis of 14 Cases.
OBJECTIVES Budd-Chiari syndrome is a low-prevalence, life-threatening disorder characterized by hepatic venous outflow obstruction at the hepatic venules, the large hepatic veins, the inferior vena cava, or the right atrium. Orthotopic liver transplant should be considered for patients with fulminant and chronic forms of the syndrome. MATERIALS AND METHODS Fourteen patients received 15 orthot...
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ورودعنوان ژورنال:
- Experimental and clinical transplantation : official journal of the Middle East Society for Organ Transplantation
دوره 10 2 شماره
صفحات -
تاریخ انتشار 2012